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Idiopathic ventricular fibrillation in two infants, not always idiopathic on follow-up

      Idiopathic ventricular fibrillation (IVF) is defined as spontaneous ventricular fibrillation (VF) in the absence of identifiable cardiac and extracardiac abnormalities responsible for the arrhythmic event.
      Survivors of out-of-hospital cardiac arrest with apparently normal heart
      Need for definition and standardized clinical evaluation Consensus Statement of the Joint Steering Committees of the Unexplained Cardiac Arrest Registry of Europe and of the Idiopathic Ventricular Fibrillation Registry of the United States.
      IVF accounts for 5% to 10% of out-of-hospital survivors of cardiac arrest.
      • Belhassen B.
      • Viskin S.
      Idiopathic ventricular tachycardia and fibrillation.
      • Meissner M.D.
      • Lehmann M.H.
      • Steinman R.T.
      • et al.
      Ventricular fibrillation in patients without significant structural heart disease: a multicenter experience with implantable cardioverter-defibrillator therapy.
      The mean age of IVF patients is 35 to 40 years, and 70% to 75% are male.
      • Marcus F.I.
      Idiopathic ventricular fibrillation.
      Implantable cardioverter defibrillator (ICD) forms the mainstay of treatment,
      Survivors of out-of-hospital cardiac arrest with apparently normal heart
      Need for definition and standardized clinical evaluation Consensus Statement of the Joint Steering Committees of the Unexplained Cardiac Arrest Registry of Europe and of the Idiopathic Ventricular Fibrillation Registry of the United States.
      and the youngest reported case of IVF is a 7-year-old boy treated with ICD.
      • Stefanelli C.B.
      • Bradley D.J.
      • Leroy S.
      • et al.
      Implantable cardioverter defibrillator therapy for life-threatening arrhythmias in young patients.

      Keywords

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